Examples of vascular malformations are port-wine stain (including Sturge-Weber syndrome) and cystic hygromas (lymphatic malformation). Sturge-Weber syndrome is a facial port-wine stain that can involve the brain and produce glaucoma or seizures. It needs to be evaluated closely by a pediatric plastic surgeon as well as a neurologist.
Lymphatic malformations can interfere with the body’s ability to remove bacteria from body tissues. Vascular malformations affect boys and girls at the same rate. Although present at birth, they may not be detected in utero.
Vascular anomalies do not go away without treatment and unfortunately do not respond to steroids, interferon or other medication therapies. Vascular laser treatments are excellent for treating vascular malformations. Because these grow throughout life, they require multiple treatments with the laser.
We frequently work with a pediatric radiologist to optimize the treatment of these lesions when surgery is required. We may order an MRI study and a special blood vessel study to evaluate the lymphangioma or vascular malformation prior to any therapy.
Prior to surgery, we will consult the interventional radiology unit for either percutaneous sclerotherapy or intravascular embolization, which decreases the size of the lesion and the amount of bleeding. Using a multidisciplinary approach reduces the number of surgeries needed and the amount of overall scaring.